NCBI Accession #
XP_015620588.1
NCBI GenBank Nucleotide #
XM_015765102.1
NCBI Official Full Name
methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial
NCBI Official Symbol
LOC4352741
NCBI Official Synonym Symbols
MCCA; OsJ_36794
NCBI Protein Information
methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial
UniProt Synonym Gene Names
MCCase subunit alpha
UniProt Protein Name
Methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial
UniProt Synonym Protein Names
3-methylcrotonyl-CoA carboxylase 1; 3-methylcrotonyl-CoA:carbon dioxide ligase subunit alpha
UniProt Primary Accession #
Q2QMG2
UniProt Secondary Accession #
Q0IM20; Q2QMG3; Q2QMG4; Q8W2G0; A0A0P0YC98
UniProt Related Accession #
Q2QMG2
UniProt Comments
Biotin-attachment subunit of the 3-methylcrotonyl-CoA carboxylase, an enzyme that catalyzes the conversion of 3-methylcrotonyl-CoA to 3-methylglutaconyl-CoA, a critical step for leucine and isovaleric acid catabolism.