NCBI Accession #
NP_001105895.1
NCBI GenBank Nucleotide #
NM_001112425.1
NCBI Official Full Name
lon protease homolog, mitochondrial
NCBI Official Symbol
LON2
NCBI Official Synonym Symbols
GRMZM2G113056
NCBI Protein Information
lon protease homolog, mitochondrial
UniProt Protein Name
Lon protease homolog, mitochondrial
UniProt Primary Accession #
P93648
UniProt Related Accession #
P93648
UniProt Comments
ATP-dependent serine protease that mediates the selective degradation of misfolded, unassembled or oxidatively damaged polypeptides as well as certain short-lived regulatory proteins in the mitochondrial matrix. May also have a chaperone function in the assembly of inner membrane protein complexes. Participates in the regulation of mitochondrial gene expression and in the maintenance of the integrity of the mitochondrial genome. Binds to mitochondrial DNA in a site-specific manner.