NCBI Accession #
NP_001275043.1
NCBI GenBank Nucleotide #
NM_001288114.1
NCBI Official Full Name
2-methylacyl-CoA dehydrogenase, mitochondrial
NCBI Official Symbol
LOC102589539
NCBI Official Synonym Symbols
ivd1; 2MBCD; St-IVD1
NCBI Protein Information
2-methylacyl-CoA dehydrogenase, mitochondrial
UniProt Synonym Gene Names
IVD1; 2MBCD; St-IVD1
UniProt Protein Name
2-methylacyl-CoA dehydrogenase, mitochondrial
UniProt Synonym Protein Names
2-methylbutyryl-CoA deshydrogenase; 2MBCD; Isovaleryl-CoA dehydrogenase 1; St-IVD1
UniProt Primary Accession #
Q9FS88
UniProt Secondary Accession #
M1CK01
UniProt Related Accession #
Q9FS88
UniProt Comments
Short/branched-chain acyl-CoA dehydrogenase (SBCAD). Uses 2-methylbutanoyl-CoA as substrate. Minor activity with the straight-chain substrates, butyryl-CoA, valeryl-CoA, hexanoyl-CoA, and octanoyl-CoA but no activity with isovaleryl-CoA.