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Glucosamine (N-acetyl)-6-Sulfatase/GNS Antibody
SPA-04505
| Size | Price |
| 100 µL | Online Inquiry |
| 20 µL | Online Inquiry |
| More Options | Online Inquiry |
| Target Information | |
|---|---|
| Target Name | Glucosamine (N-acetyl)-6-Sulfatase |
| Gene Abbr. | GNS |
| Gene ID | 2799 |
| Full Name | glucosamine (N-acetyl)-6-sulfatase |
| Alias | G6S |
| Introduction | GNS is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparin sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder ucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome. |
| Product Details | |
|---|---|
| Host | Rabbit |
| Clonality | Monoclonal |
| Clone No. | 7 |
| Isotype | IgG |
| Immunogen | This antibody was obtained from a rabbit immunized with purified, recombinant Human Glucosamine (N-acetyl)-6-Sulfatase/GNS (NP_002067.1; Met 1-Leu 552). |
| Usage | |
|---|---|
| Application | WB, ELISA |
| Dilutions | Western Blot (1:500-1:2000); ELISA (1:5000-1:10000) |
| Reactivity | Human |
| Storage & Handling | |
|---|---|
| Storage Buffer | 0.2 µm filtered solution in PBS. |
| Preservative | No Preservative |
| Storage Temp. | Store at 4 °C for a short term. Aliquot and store at -20 °C for long-term storage. |
| Handling | Avoid freeze-thaw cycles. |
For research use only. Not intended for any clinical use. No products from CD BioSciences may be resold, modified for resale or used to manufacture commercial products without prior written approval from CD BioSciences.